Solitary Fibrous Tumor/Hemangiopericytoma: A Companion Case Discussion of a Spectrum of Rare CNS Mesenchymal Tumors and Their Evolving WHO Classification
The combined term solitary fibrous tumor/hemangiopericytoma was recently introduced in the World Health Organization Classification of Tumors of the Central Nervous System 2016 revision. The consolidation came amid mounting evidence that these 2 mesenchymal tumors are closely related,
or even identical, entities. These neoplasms demonstrate significant clinical and demographic overlap, often indistinguishable imaging features, and a shared nerve growth factor inducible-A-binding protein 2/signal transducer and activator of transcription 6 gene fusion. We presented 2 cases
of this uncommon entity and discussed its evolving tumor classification.
Keywords: ECA = external carotid artery; HPC = hemangiopericytoma; MMA = middle meningeal artery; NAB2 = nerve growth factor inducible-A-binding protein 2; SFT = solitary fibrous tumor; STA = superficial temporal artery; STAT6 = signal transducer and activator of transcription 6; WHO = World Health Organization
Document Type: Research Article
Publication date: 01 June 2018
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