Multimodality Imaging of Cerebral Crystal-Storing Histiocytosis: Distinguishing Imaging Characteristics and a Literature Review of a Very Rare Entity
Crystal-storing histiocytosis is a rare immunoglobulin storage disorder most frequently associated with lymphoproliferative diseases and characterized by intracytoplasmic accumulations of fibrillar and crystalloid inclusions. The inclusions have been described in a variety of anatomic
sites but with only a few reported cases of CNS involvement. We presented 2 patients with cerebral crystal-storing histiocytosis and described the imaging characteristics that may distinguish brain parenchymal involvement by crystal-storing histiocytosis from other, more commonly encountered
mass lesions.
Keywords: CSH = crystal-storing histiocytosis
Document Type: Research Article
Publication date: February 1, 2019
This article was made available online on December 18, 2018 as a Fast Track article with title: "Multimodality Imaging of Cerebral Crystal-Storing Histiocytosis: Distinguishing Imaging Characteristics and a Literature Review of a Very Rare Entity".
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