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Free Content Multimodality Imaging of Cerebral Crystal-Storing Histiocytosis: Distinguishing Imaging Characteristics and a Literature Review of a Very Rare Entity

Crystal-storing histiocytosis is a rare immunoglobulin storage disorder most frequently associated with lymphoproliferative diseases and characterized by intracytoplasmic accumulations of fibrillar and crystalloid inclusions. The inclusions have been described in a variety of anatomic sites but with only a few reported cases of CNS involvement. We presented 2 patients with cerebral crystal-storing histiocytosis and described the imaging characteristics that may distinguish brain parenchymal involvement by crystal-storing histiocytosis from other, more commonly encountered mass lesions.

Keywords: CSH = crystal-storing histiocytosis

Document Type: Research Article

Publication date: February 1, 2019

This article was made available online on December 18, 2018 as a Fast Track article with title: "Multimodality Imaging of Cerebral Crystal-Storing Histiocytosis: Distinguishing Imaging Characteristics and a Literature Review of a Very Rare Entity".

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